Adrenocortical carcinoma, hereditary
Your Results
Sign InDescription
Adrenocortical carcinoma (ADCC) is a rare but aggressive childhood tumor, representing about 0.4% of childhood tumors, with a high incidence of associated tumors. ADCC occurs with increased frequency in patients with the Beckwith-Wiedemann syndrome (130650) and is a component tumor in Li-Fraumeni syndrome (LFS; 151623).
Mode of Inheritance
- Autosomal dominant inheritance
VARIANTS
11