Diffuse interstitial pulmonary fibrosis
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Sign InDescription
Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
Mode of Inheritance
VARIANTS
1
External Links
OMIM
Orphanet
HPO
Medgen